Nuclear and Neuropil Aggregates in Huntington’s Disease: Relationship to Neuropathology

Table 1.

Case information

Case Age (years) Sex PMI (hr) Pathology
HD1 29 F 6 HD grade 1
HD2 82 F 17.4 HD grade 1
HD3 40 M 12 HD grade 1
HD4 46 F 20 HD grade 2
HD5 74 M 12.5 HD grade 2
HD6 86 M 2 HD grade 3
HD7 NA M 7 HD grade 4
HD8 47 M 3.5 HD grade 4
HD9 78 F 10 HD grade 3–4
HD10 42 F 13 HD grade 3–4
HD11 17 M 5 JHD grade 4
HD12 22 M 3 JHD grade 4
CT1 68 F 3 Control
CT2 31 M 26 Control
CT3 60 M 20 Control
CT4 64 M 11 Control
ND1 NA F 4 AD
ND2 67 M 16 AD
ND3 78 M 14 AD
ND4 71 M 5 PD
ND5 77 M 10 MS
ND6 69 M 14 Multiple infarcts
ND7 53 M 7 Schizophrenia
  • PMI, Postmortem interval time; HD, Huntington’s disease; AD, Alzheimer’s disease; PD, Parkinson’s disease; MS, multiple sclerosis; ND, not determined.

  1. The Journal of Neuroscience vol. 19 no. 7 2522-2534
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