Neurobiology of Disease:A Mouse Model of Classical Late-Infantile Neuronal Ceroid Lipofuscinosis Based on Targeted Disruption of the CLN2 Gene Results
in a Loss of Tripeptidyl-Peptidase I Activity and Progressive Neurodegeneration
David E. Sleat,
Jennifer A. Wiseman,
Mukarram El-Banna,
Kwi-Hye Kim,
Qinwen Mao,
Sandy Price,
Shannon L. Macauley,
Richard L. Sidman,
Michael M. Shen,
Qi Zhao,
Marco A. Passini,
Beverly L. Davidson,
Gregory R. Stewart,
and Peter Lobel
The Journal of Neuroscience,13 October 2004, 24(41):9117-9126; doi:10.1523/JNEUROSCI.2729-04.2004
