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  1. Research Articles - Neurobiology of Disease: Disrupting the Balance of Protein Quality Control Protein UBQLN2 Accelerates Tau Proteinopathy
    • Julia E. Gerson,
    • Stephanie Sandoval-Pistorius,
    • Jacqueline P. Welday,
    • Aleija Rodriguez,
    • Jordan D. Gregory,
    • Nyjerus Liggans,
    • Kylie Schache,
    • Xingli Li,
    • Hanna Trzeciakiewicz,
    • Sami Barmada,
    • Lisa M. Sharkey,
    • and Henry L. Paulson
    The Journal of Neuroscience, 2 March 2022, 42(9):1845-1863; published ahead of print January 26, 2022, doi:10.1523/JNEUROSCI.1116-21.2021
  2. Research Articles - Neurobiology of Disease: Impaired Oligodendrocyte Maturation Is an Early Feature in SCA3 Disease Pathogenesis
    • Kristen H. Schuster,
    • Annie J. Zalon,
    • Hongjiu Zhang,
    • Danielle M. DiFranco,
    • Nicholas R. Stec,
    • Zaid Haque,
    • Kate G. Blumenstein,
    • Amanda M. Pierce,
    • Yuanfang Guan,
    • Henry L. Paulson,
    • and Hayley S. McLoughlin
    The Journal of Neuroscience, 23 February 2022, 42(8):1604-1617; published ahead of print January 18, 2022, doi:10.1523/JNEUROSCI.1954-20.2021
  3. Articles - Cellular/Molecular: Loss of F-box Only Protein 2 (Fbxo2) Disrupts Levels and Localization of Select NMDA Receptor Subunits, and Promotes Aberrant Synaptic Connectivity
    • Graham Atkin,
    • Shannon Moore,
    • Yuan Lu,
    • Rick F. Nelson,
    • Nathan Tipper,
    • Gautam Rajpal,
    • Jack Hunt,
    • William Tennant,
    • Johannes W. Hell,
    • Geoffrey G. Murphy,
    • and Henry Paulson
    The Journal of Neuroscience, 15 April 2015, 35(15):6165-6178; doi:10.1523/JNEUROSCI.3013-14.2015
  4. Articles - Neurobiology of Disease: Differential Effects of Delayed Aging on Phenotype and Striatal Pathology in a Murine Model of Huntington Disease
    • Sara J. Tallaksen-Greene,
    • Marianna Sadagurski,
    • Li Zeng,
    • Roseanne Mauch,
    • Matthew Perkins,
    • Varuna C. Banduseela,
    • Andrew P. Lieberman,
    • Richard A. Miller,
    • Henry L. Paulson,
    • and Roger L. Albin
    The Journal of Neuroscience, 19 November 2014, 34(47):15658-15668; doi:10.1523/JNEUROSCI.1830-14.2014
  5. Articles - Neurobiology of Disease: Early Changes in Cerebellar Physiology Accompany Motor Dysfunction in the Polyglutamine Disease Spinocerebellar Ataxia Type 3
    • Vikram G. Shakkottai,
    • Maria do Carmo Costa,
    • James M. Dell'Orco,
    • Ananthakrishnan Sankaranarayanan,
    • Heike Wulff,
    • and Henry L. Paulson
    The Journal of Neuroscience, 7 September 2011, 31(36):13002-13014; doi:10.1523/JNEUROSCI.2789-11.2011
  6. Articles - Neurobiology of Disease: Selective Cochlear Degeneration in Mice Lacking the F-Box Protein, Fbx2, a Glycoprotein-Specific Ubiquitin Ligase Subunit
    • Rick F. Nelson,
    • Kevin A. Glenn,
    • Yuzhou Zhang,
    • Hsiang Wen,
    • Tina Knutson,
    • Cynthia M. Gouvion,
    • Barbara K. Robinson,
    • Zouping Zhou,
    • Baoli Yang,
    • Richard J. H. Smith,
    • and Henry L. Paulson
    The Journal of Neuroscience, 9 May 2007, 27(19):5163-5171; doi:10.1523/JNEUROSCI.0206-07.2007
  7. Neurobiology of Disease: Silencing Primary Dystonia: Lentiviral-Mediated RNA Interference Therapy for DYT1 Dystonia
    • Pedro Gonzalez-Alegre,
    • Nicole Bode,
    • Beverly L. Davidson,
    • and Henry L. Paulson
    The Journal of Neuroscience, 9 November 2005, 25(45):10502-10509; doi:10.1523/JNEUROSCI.3016-05.2005
  8. Neurobiology of Disease: CHIP Suppresses Polyglutamine Aggregation and Toxicity In Vitro and In Vivo
    • Victor M. Miller,
    • Rick F. Nelson,
    • Cynthia M. Gouvion,
    • Aislinn Williams,
    • Edgardo Rodriguez-Lebron,
    • Scott Q. Harper,
    • Beverly L. Davidson,
    • Michael R. Rebagliati,
    • and Henry L. Paulson
    The Journal of Neuroscience, 5 October 2005, 25(40):9152-9161; doi:10.1523/JNEUROSCI.3001-05.2005
  9. Neurobiology of Disease: Aberrant Cellular Behavior of Mutant TorsinA Implicates Nuclear Envelope Dysfunction in DYT1 Dystonia
    • Pedro Gonzalez-Alegre and
    • Henry L. Paulson
    The Journal of Neuroscience, 17 March 2004, 24(11):2593-2601; doi:10.1523/JNEUROSCI.4461-03.2004
  10. ARTICLE - Cellular/Molecular: Analysis of the Role of Heat Shock Protein (Hsp) Molecular Chaperones in Polyglutamine Disease
    • Yaohui Chai,
    • Stacia L. Koppenhafer,
    • Nancy M. Bonini,
    • and Henry L. Paulson
    The Journal of Neuroscience, 1 December 1999, 19(23):10338-10347; doi:10.1523/JNEUROSCI.19-23-10338.1999
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